{"id":55,"date":"2021-07-12T12:44:04","date_gmt":"2021-07-12T10:44:04","guid":{"rendered":"http:\/\/crmw.fr\/?page_id=55"},"modified":"2021-07-12T12:48:10","modified_gmt":"2021-07-12T10:48:10","slug":"filiere-mhemo","status":"publish","type":"page","link":"https:\/\/crmw.fr\/?page_id=55","title":{"rendered":"La Fili\u00e8re de sant\u00e9 MHEMO"},"content":{"rendered":"\n<p>La fili\u00e8re de sant\u00e9 des maladies H\u00e9morragiques constitutionnelles (MHEMO) a \u00e9t\u00e9 &nbsp;cr\u00e9\u00e9e en d\u00e9cembre 2014 dans le cadre du 2<sup>\u00e8me<\/sup>&nbsp;Plan National Maladies Rares&nbsp; (PNMR2). Sa labellisation a \u00e9t\u00e9 renouvel\u00e9e en juin 2019 dans le cadre du 3\u00e8me Plan National Maladies Rares&nbsp; (PNMR3).<\/p>\n\n\n\n<p>Elle regroupe les acteurs \u0153uvrant dans le domaine des maladies h\u00e9morragiques familiales :<\/p>\n\n\n\n<ul class=\"wp-block-list\"><li><strong>3<\/strong>\u00a0Centres de\u00a0R\u00e9f\u00e9rence\u00a0Maladies Rares (CRMR) :<ul><li><strong>CRH\u00a0<\/strong>:\u00a0<strong>Centre de R\u00e9f\u00e9rence de l\u2019H\u00e9mophilie et autres\u00a0 d\u00e9ficits constitutionnels en prot\u00e9ines de la coagulation<\/strong>\u00a0(Coordonnateur : Pr\u00a0 Claude NEGRIER \u2013 Lyon).<br>Les maladies prises en charge par le CRH sont\u00a0<strong><a href=\"https:\/\/mhemo.fr\/les-pathologies\/lhemophilie\/\">l\u2019h\u00e9mophilie A et B<\/a><\/strong>\u00a0et les\u00a0<strong><a href=\"https:\/\/mhemo.fr\/les-pathologies\/les-deficits-rares-en-facteurs-de-la-coagulation\/\">autres d\u00e9ficits rares en facteur de la coagulation<\/a><\/strong>.\u00a0Le CRH est compos\u00e9 d\u2019un site coordonnateur et de 2 sites constitutifs \u00a0associ\u00e9s au centre de r\u00e9f\u00e9rence (Kremlin Bic\u00eatre \u2013 Nantes)<\/li><\/ul><ul><li><strong>CRMW<\/strong>\u00a0:\u00a0<strong>Centre de R\u00e9f\u00e9rence de la Maladie de Willebrand<\/strong>\u00a0(Coordonnateur : Pr Sophie SUSEN \u2013 Lille)<br>Les maladies prises en charge par le CRMW sont les diverses formes de\u00a0<strong>maladies de Willebrand<\/strong>\u00a0constitutionnelles ainsi que les formes acquises de la maladie. Le CRMW est compos\u00e9\u00a0d\u2019un site coordonnateur et\u00a0de 2 sites constitutifs associ\u00e9s au centre de r\u00e9f\u00e9rence (Caen \u2013 Paris Lariboisi\u00e8re)<\/li><\/ul><ul><li><strong>CRPP<\/strong>\u00a0:\u00a0<strong>Centre de R\u00e9f\u00e9rence des Pathologies Plaquettaires constitutionnelles<\/strong>\u00a0(Coordonnateur : Pr Marie-Christine ALESSI \u2013 Marseille)<br>Les maladies prises en charge par le CRPP sont\u00a0les <a href=\"https:\/\/maladies-plaquettes.org\/\"><strong>thrombopathies et thrombop\u00e9nies familiales<\/strong><\/a>. Le CRPP est compos\u00e9\u00a0d\u2019un site coordonnateur et\u00a0de 3 sites constitutifs associ\u00e9s au centre de r\u00e9f\u00e9rence (Toulouse \u2013 Paris Trousseau \u2013 Bordeaux).<\/li><\/ul><\/li><\/ul>\n\n\n\n<ul class=\"wp-block-list\"><li><strong>30<\/strong>&nbsp;Centres de Ressources et de Comp\u00e9tences Maladies h\u00e9morragiques Constitutionnelles (CRC-MHC)&nbsp;<sup>1<\/sup><\/li><li><strong>6<\/strong>&nbsp;Centres de Traitement des Maladies H\u00e9morragiques Constitutionnelles (CT-MHC)&nbsp;<sup>2<\/sup><\/li><li>Plusieurs consultations d\u2019h\u00e9mostase dans des h\u00f4pitaux p\u00e9riph\u00e9rique<\/li><li><strong>1<\/strong>&nbsp;association de patient : Association fran\u00e7aise des h\u00e9mophiles (AFH)<\/li><li><strong>17<\/strong>&nbsp;laboratoires de biologie mol\u00e9culaire constituant le r\u00e9seau&nbsp;GENOSTASE,&nbsp;r\u00e9seau national des laboratoires r\u00e9alisant les caract\u00e9ristiques g\u00e9n\u00e9tiques des maladies constitutionnelles de la coagulation et de la fibrinolyse<\/li><li><strong>35<\/strong>&nbsp;laboratoires d\u2019h\u00e9mostase<\/li><li><strong>13<\/strong>&nbsp;unit\u00e9s de recherche<\/li><li><strong>1<\/strong>&nbsp;Base de donn\u00e9es support des \u00e9tudes \u00e9pid\u00e9miologiques : le&nbsp;<strong><a href=\"https:\/\/mhemo.fr\/la-filiere-mhemo\/le-reseau-francecoag\/la-cohorte-francecoag\/\">R\u00e9seau FranceCoag<\/a><\/strong><\/li><li><strong>7<\/strong>&nbsp;soci\u00e9t\u00e9s savantes :<ul><li><strong><a href=\"http:\/\/sfh.hematologie.net\">SFH (Soci\u00e9t\u00e9 Fran\u00e7aise d\u2019H\u00e9matologie)<\/a><\/strong><\/li><li><strong><a href=\"http:\/\/site.geht.org\/\">GFHT (Groupe Fran\u00e7ais d\u2019\u00e9tude sur l\u2019H\u00e9mostase et le Thrombose)<\/a><\/strong><\/li><li><strong><a href=\"http:\/\/www.sitedelaship.fr\/\">SHIP (Soci\u00e9t\u00e9 fran\u00e7aise d\u2019H\u00e9matologie et d\u2019Immunologie P\u00e9diatrique)<\/a><\/strong><\/li><li><strong><a href=\"https:\/\/www.isth.org\/\">ISTH (International Society on Thrombosis and Haemostasis)<\/a><\/strong><\/li><li><strong><a href=\"http:\/\/eahad.org\/\">EAHAD (European Association for Haemophilia and Allied Disorders)<\/a><\/strong><\/li><li><strong><a rel=\"noreferrer noopener\" href=\"https:\/\/www.wfh.org\/en\/home\" target=\"_blank\">WFH (World Federation of Haemophilia)<\/a><\/strong><\/li><\/ul><\/li><\/ul>\n","protected":false},"excerpt":{"rendered":"<p>La fili\u00e8re de sant\u00e9 des maladies H\u00e9morragiques constitutionnelles (MHEMO) a \u00e9t\u00e9 &nbsp;cr\u00e9\u00e9e en d\u00e9cembre 2014 dans le cadre du 2\u00e8me&nbsp;Plan<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":91,"menu_order":1,"comment_status":"closed","ping_status":"closed","template":"","meta":{"colormag_page_container_layout":"default_layout","colormag_page_sidebar_layout":"default_layout","footnotes":""},"class_list":["post-55","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/crmw.fr\/index.php?rest_route=\/wp\/v2\/pages\/55","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/crmw.fr\/index.php?rest_route=\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/crmw.fr\/index.php?rest_route=\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/crmw.fr\/index.php?rest_route=\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/crmw.fr\/index.php?rest_route=%2Fwp%2Fv2%2Fcomments&post=55"}],"version-history":[{"count":8,"href":"https:\/\/crmw.fr\/index.php?rest_route=\/wp\/v2\/pages\/55\/revisions"}],"predecessor-version":[{"id":931,"href":"https:\/\/crmw.fr\/index.php?rest_route=\/wp\/v2\/pages\/55\/revisions\/931"}],"up":[{"embeddable":true,"href":"https:\/\/crmw.fr\/index.php?rest_route=\/wp\/v2\/pages\/91"}],"wp:attachment":[{"href":"https:\/\/crmw.fr\/index.php?rest_route=%2Fwp%2Fv2%2Fmedia&parent=55"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}