{"id":55,"date":"2021-07-12T12:44:04","date_gmt":"2021-07-12T10:44:04","guid":{"rendered":"http:\/\/crmw.fr\/?page_id=55"},"modified":"2026-08-13T13:05:55","modified_gmt":"2026-08-13T11:05:55","slug":"filiere-mhemo","status":"publish","type":"page","link":"https:\/\/crmw.fr\/?page_id=55","title":{"rendered":"La Fili\u00e8re de sant\u00e9 MHEMO"},"content":{"rendered":"\n<p class=\"wp-block-paragraph\">La fili\u00e8re de sant\u00e9 des maladies H\u00e9morragiques constitutionnelles (MHEMO) a \u00e9t\u00e9 &nbsp;cr\u00e9\u00e9e en d\u00e9cembre 2014 dans le cadre du 2<sup>\u00e8me<\/sup>&nbsp;Plan National Maladies Rares&nbsp; (PNMR2). Sa labellisation a \u00e9t\u00e9 renouvel\u00e9e en janvier 2025 dans le cadre du 3\u00e8me Plan National Maladies Rares&nbsp; (PNMR4).<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Elle regroupe les acteurs \u0153uvrant dans le domaine des maladies h\u00e9morragiques familiales :<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>3<\/strong>&nbsp;Centres de&nbsp;R\u00e9f\u00e9rence&nbsp;Maladies Rares (CRMR) :\n<ul class=\"wp-block-list\">\n<li><strong>CRH&nbsp;<\/strong>:&nbsp;<strong>Centre de R\u00e9f\u00e9rence de l\u2019H\u00e9mophilie et autres&nbsp; d\u00e9ficits constitutionnels en prot\u00e9ines de la coagulation<\/strong>&nbsp;(Coordonnateur : Pr&nbsp; Yesim Dargaud \u2013 Lyon).<br>Les maladies prises en charge par le CRH sont&nbsp;<strong><a href=\"https:\/\/mhemo.fr\/les-pathologies\/lhemophilie\/\">l\u2019h\u00e9mophilie A et B<\/a><\/strong>&nbsp;et les&nbsp;<strong><a href=\"https:\/\/mhemo.fr\/les-pathologies\/les-deficits-rares-en-facteurs-de-la-coagulation\/\">autres d\u00e9ficits rares en facteur de la coagulation<\/a><\/strong>.&nbsp;Le CRH est compos\u00e9 d\u2019un site coordonnateur et de 3 sites constitutifs &nbsp;associ\u00e9s au centre de r\u00e9f\u00e9rence (Kremlin Bic\u00eatre \u2013 Necker &#8211; Rennes)<\/li>\n\n\n\n<li><strong>CRMW<\/strong>&nbsp;:&nbsp;<strong>Centre de R\u00e9f\u00e9rence de la Maladie de Willebrand<\/strong>&nbsp;(Coordonnateur : Pr Sophie SUSEN \u2013 Lille)<br>Les maladies prises en charge par le CRMW sont les diverses formes de&nbsp;<strong>maladies de Willebrand<\/strong>&nbsp;constitutionnelles ainsi que les formes acquises de la maladie. Le CRMW est compos\u00e9&nbsp;d\u2019un site coordonnateur et&nbsp;de 3 sites constitutifs associ\u00e9s au centre de r\u00e9f\u00e9rence (Caen \u2013 Nantes &#8211; Paris Lariboisi\u00e8re)<\/li>\n\n\n\n<li><strong>CRPP<\/strong>&nbsp;:&nbsp;<strong>Centre de R\u00e9f\u00e9rence des Pathologies Plaquettaires constitutionnelles<\/strong>&nbsp;(Coordonnateur : Pr Paul Saultier \u2013 Marseille)<br>Les maladies prises en charge par le CRPP sont&nbsp;les <a href=\"https:\/\/maladies-plaquettes.org\/\"><strong>thrombopathies et thrombop\u00e9nies familiales<\/strong><\/a>. Le CRPP est compos\u00e9&nbsp;d\u2019un site coordonnateur et&nbsp;de 3 sites constitutifs associ\u00e9s au centre de r\u00e9f\u00e9rence (Toulouse \u2013 Paris Trousseau \u2013 Bordeaux).<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>32<\/strong>\u00a0Centres de Ressources et de Comp\u00e9tences Maladies h\u00e9morragiques Rares (CRC-MHR)\u00a0<sup>1<\/sup><\/li>\n\n\n\n<li><strong>5<\/strong>\u00a0Centres de Traitement des Maladies H\u00e9morragiques Rares (CT-MHR)\u00a0<sup>2<\/sup><\/li>\n\n\n\n<li>Plusieurs consultations d\u2019h\u00e9mostase dans des h\u00f4pitaux p\u00e9riph\u00e9rique<\/li>\n\n\n\n<li><strong>1<\/strong>&nbsp;association de patient : Association fran\u00e7aise des h\u00e9mophiles (AFH)<\/li>\n\n\n\n<li><strong>15<\/strong>&nbsp;laboratoires de biologie mol\u00e9culaire constituant le r\u00e9seau&nbsp;GENOSTASE,&nbsp;r\u00e9seau national des laboratoires r\u00e9alisant les caract\u00e9ristiques g\u00e9n\u00e9tiques des maladies constitutionnelles de la coagulation et de la fibrinolyse<\/li>\n\n\n\n<li><strong>42<\/strong>&nbsp;laboratoires d\u2019h\u00e9mostase<\/li>\n\n\n\n<li><strong>1<\/strong>&nbsp;Base de donn\u00e9es support des \u00e9tudes \u00e9pid\u00e9miologiques : le&nbsp;<strong><a href=\"https:\/\/mhemo.fr\/la-filiere-mhemo\/le-reseau-francecoag\/la-cohorte-francecoag\/\">R\u00e9seau FranceCoag<\/a><\/strong><\/li>\n\n\n\n<li>6&nbsp;soci\u00e9t\u00e9s savantes :\n<ul class=\"wp-block-list\">\n<li><strong><a href=\"http:\/\/sfh.hematologie.net\">SFH (Soci\u00e9t\u00e9 Fran\u00e7aise d\u2019H\u00e9matologie)<\/a><\/strong><\/li>\n\n\n\n<li><a href=\"https:\/\/sfth.fr\/presentation-du-sfth\/\" data-type=\"link\" data-id=\"https:\/\/sfth.fr\/presentation-du-sfth\/\"><strong>SFTH (Soci\u00e9t\u00e9 Fran\u00e7aise de Thrombose et d\u2019H\u00e9mostase<\/strong><\/a><\/li>\n\n\n\n<li><strong><a href=\"http:\/\/www.sitedelaship.fr\/\">SHIP (Soci\u00e9t\u00e9 fran\u00e7aise d\u2019H\u00e9matologie et d\u2019Immunologie P\u00e9diatrique)<\/a><\/strong><\/li>\n\n\n\n<li><strong><a href=\"https:\/\/www.isth.org\/\">ISTH (International Society on Thrombosis and Haemostasis)<\/a><\/strong><\/li>\n\n\n\n<li><strong><a href=\"http:\/\/eahad.org\/\">EAHAD (European Association for Haemophilia and Allied Disorders)<\/a><\/strong><\/li>\n\n\n\n<li><strong><a href=\"https:\/\/www.wfh.org\/en\/home\" target=\"_blank\" rel=\"noreferrer noopener\">WFH (World Federation of Haemophilia)<\/a><\/strong><\/li>\n<\/ul>\n<\/li>\n<\/ul>\n\n\n\n<p class=\"wp-block-paragraph\"><\/p>\n","protected":false},"excerpt":{"rendered":"<p>La fili\u00e8re de sant\u00e9 des maladies H\u00e9morragiques constitutionnelles (MHEMO) a \u00e9t\u00e9 &nbsp;cr\u00e9\u00e9e en d\u00e9cembre 2014 dans le cadre du 2\u00e8me&nbsp;Plan<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":91,"menu_order":1,"comment_status":"closed","ping_status":"closed","template":"","meta":{"colormag_page_container_layout":"default_layout","colormag_page_sidebar_layout":"default_layout","footnotes":""},"class_list":["post-55","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/crmw.fr\/index.php?rest_route=\/wp\/v2\/pages\/55","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/crmw.fr\/index.php?rest_route=\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/crmw.fr\/index.php?rest_route=\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/crmw.fr\/index.php?rest_route=\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/crmw.fr\/index.php?rest_route=%2Fwp%2Fv2%2Fcomments&post=55"}],"version-history":[{"count":16,"href":"https:\/\/crmw.fr\/index.php?rest_route=\/wp\/v2\/pages\/55\/revisions"}],"predecessor-version":[{"id":1541,"href":"https:\/\/crmw.fr\/index.php?rest_route=\/wp\/v2\/pages\/55\/revisions\/1541"}],"up":[{"embeddable":true,"href":"https:\/\/crmw.fr\/index.php?rest_route=\/wp\/v2\/pages\/91"}],"wp:attachment":[{"href":"https:\/\/crmw.fr\/index.php?rest_route=%2Fwp%2Fv2%2Fmedia&parent=55"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}